Leiomyosarcoma of the Superficial Femoral vein – A rare tumor at an unusual site.

Abstract

Background: The leiomyosarcomas most commonly arise from smooth muscles of the uterus and gastrointestinal tract. The vascular origin of the leiomyosarcoma is very rare; however, veins are more frequently affected in such cases.

Case Presentation: A 23-year-old boy presents with left thigh painless swelling. Subsequently, he underwent multimodality radiological examinations, which showed left superficial femoral vein mass, which later on histopathological evaluation came out to be grade III leiomyosarcoma of the superficial femoral vein.

Management & Results: The patient was given chemotherapy, but unfortunately, after three cycles of chemotherapy patient developed pulmonary metastases. Currently, the patient is under palliative treatment.

Conclusion: Primary vascular leiomyosarcomas are very rare entities. The knowledge of these rare tumors is essential for the reporting radiologists and clinicians to properly diagnose these aggressive tumors to prevent any delays in the management.